Challenges in the management of caudal duplication syndrome

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dc.contributor.authorBeķere, Laine
dc.contributor.authorĢīlis, Ainārs
dc.contributor.authorĀbola, Zane
dc.contributor.authorLidaka, Lasma
dc.contributor.institutionDepartment of Pathology
dc.date.accessioned2022-01-24T22:10:01Z
dc.date.available2022-01-24T22:10:01Z
dc.date.issued2021-12
dc.description.abstractCaudal duplication syndrome (CDS) is a rare developmental anomaly in which embryonic cloaca and notochord structures are duplicated [1]. Due to the diverse clinical manifestation and rarity of CDS, it is crucial to report every case and to share experience and outcomes of individually adjusted management plans. We report here the case of a 2-year-old girl born with duplication of the urogenital (bladder, urethra, uterus, vagina, vulva) and gastrointestinal (gallbladder, appendix vermiformis) systems. Additionally, coccygeal agenesis, lipomyelomeningocele and vertical talus were present. A thorough examination and urological reconstructive surgery were performed. While there may be a desire from patients, parents and healthcare specialists to modify all malformations to an anatomically correct state, the current opinion is that only anatomical variants that influence function should be modified. Consent from patients should be sought for decisions regarding more sensitive matters such as vulva surgery for cosmetic reasons or correction of anatomical variants without functional consequences.en
dc.description.statusPeer reviewed
dc.format.extent7
dc.format.extent3806103
dc.identifier.citationBeķere, L, Ģīlis, A, Ābola, Z & Lidaka, L 2021, 'Challenges in the management of caudal duplication syndrome', Journal of Pediatric Surgery Case Reports, vol. 75, 102083. https://doi.org/10.1016/j.epsc.2021.102083
dc.identifier.doi10.1016/j.epsc.2021.102083
dc.identifier.issn2213-5766
dc.identifier.urihttps://dspace.rsu.lv/jspui/handle/123456789/7276
dc.identifier.urlhttps://www-webofscience-com.db.rsu.lv/wos/woscc/summary/f646bf9c-d1d7-4227-a904-877d8edfb0ac-207ea1d6/relevance/1
dc.language.isoeng
dc.relation.ispartofJournal of Pediatric Surgery Case Reports
dc.rightsinfo:eu-repo/semantics/openAccess
dc.subjectCaudal duplication syndrome
dc.subjectDouble vulva
dc.subjectDouble urinary bladder
dc.subjectReconstructive surgery
dc.subject3.2 Clinical medicine
dc.subject3.1 Basic medicine
dc.subject1.1. Scientific article indexed in Web of Science and/or Scopus database
dc.titleChallenges in the management of caudal duplication syndromeen
dc.type/dk/atira/pure/researchoutput/researchoutputtypes/contributiontojournal/article

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